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TEMUAN RADIOLOGIS HIRSCHSPRUNG ASSOCIATED ENTEROCOLITIS (HAEC) PASCA PROSEDUR OPERASI SOAVE DAN DUHAMEL DI RSUP DR. SARDJITO YOGYAKARTA

AGITHA SWANDARU RASTAPUTRA, dr. Andi Dwihantoro, Sp.B, Sp.BA; dr. Gunadi, Ph.D

2016 | Skripsi | S1 PENDIDIKAN DOKTER

Latar Belakang: Hirschsprung Associated Enterocolitis (HAEC) adalah komplikasi dari Penyakit Hirschsprung yang memiliki angka morbiditas dan mortalitas yang paling tinggi. Walaupun telah diakukan terapi definitif, tetap bisa terjadi komplikasi HAEC. Untuk mencegah morbiditas dan mortalitas, dibutuhkan diagnosis HAEC sedini mungkin menggunakan skor Delphi. Skor Delphi terdiri dari komponen klinis, radiologis, dan laboratorium. Temuan radiologis meliputi dilatasi lumen usus, multiple air-fluid levels, cutoff sign, pneumatosis intestinalis, dan sawtooth appearance. Tujuan: Penelitian ini bertujuan untuk mengetahui temuan radiologis pasca prosedur operasi Soave dan Duhamel serta mengetahui perbandingan proporsi temuan radiologis pasca prosedur operasi Soave dan Duhamel. Metode: Pengambilan data berupa data sekunder dilakukan di Instalasi Catatan Medik RSUP Dr. Sardjito. Data berasal dari rekam medis pasien dengan Penyakit Hirschsprung yang telah dilakukan prosedur operasi Soave atau Duhamel. Hasil: Tidak ada perbedaan yang signifikan antara temuan dilatasi lumen usus, multiple air-fluid levels, cutoff sign, pneumatosis intestinalis, dan sawtooth appearance pasca prosedur operasi Soave dengan Duhamel. Kesimpulan: Tidak ada perbedaan proporsi temuan radiologis Hirschsprung Associated Enterocolitis yang signifikan pada pasca prosedur operasi Soave dengan Duhamel.

Background: Hirschsprung Associated Enterocolitis (HAEC) is a complication of Hirschsprung's Disease with highest morbidity and mortality rate. Although definitive therapy has been performed, HAEC could still be found. Early diagnosis of HAEC using Delphi Score is needed. Delphi Score consist of clinical, radiological, and laboratorical findings. The radiological findings are dilated bowel, multiple air-fluid levels, cutoff sign, pneumatosis intestinalis, dan sawtooth appearance. Objective: The aim of this study is to find out radiological findings post Soave and Duhamel procedure and to find out the proportion of radiological findings between post Soave procedure and post Duhamel procedure. Method: The data is secondary, taken from Instalasi Catatan Medik RSUP Dr. Sardjito in the form of medical records of patients with Hirschsprung's Disease who have undergo Soave or Duhamel procedure. Result: There is no significant difference between findings of dilated bowel, multiple air-fluid levels, cutoff sign, pneumatosis intestinalis, and sawtooth appearance post Soave surgical procedure and Duhamel surgical procedure. Conclusion: There is no significant proportions of radiological findings for Hirschsprung Associated Enterocolitis post Soave and Duhamel procedure.

Kata Kunci : Hirschsprung Associated Enterocolitis, Temuan Radiologis, Soave, Duhamel

  1. S1-2016-329261-abstract.pdf  
  2. S1-2016-329261-bibliography.pdf  
  3. S1-2016-329261-tableofcontent.pdf  
  4. S1-2016-329261-title.pdf